Correction of tricuspid atresia

Area of Science:

• Cardiovascular Surgery
• Pediatric Cardiology
• Congenital Heart Disease

Background:

• Tricuspid atresia management presents significant challenges.
• The Fontan-Baudet procedure offers a physiological correction for tricuspid atresia.
• Few successful operations have been reported since its description in 1971.

Purpose of the Study:

• To present two cases of successful Fontan-Baudet operations for tricuspid atresia.
• To discuss the management challenges and criteria for patient selection.
• To explore potential long-term complications and the role of palliative surgery.

Main Methods:

• Detailed operative procedures for two patients with tricuspid atresia are described.
• One patient had complex prior palliative surgeries; the other had no prior intervention.
• Postoperative courses and management strategies are analyzed.

Main Results:

• Successful outcomes were achieved in both patients, aged 20 and 8.
• The first patient's complex surgical history presented unique challenges.
• The second patient had an undiagnosed partial atrioventricular canal at operation.

Conclusions:

• The Fontan-Baudet operation can be successful in selected tricuspid atresia patients.
• Palliative surgery in infancy may facilitate later Fontan-Baudet correction.
• Careful patient selection and management are crucial for favorable outcomes.