[Coordination disorders in children with the Louis-Bar syndrome]

Results of anamnestic and clinico-neurological examinations of 39 children (24 boys and 15 girls aged from 4 to 16 years) with the Louis Barr syndrome are presented. Coordination disorders as the very first symptom were noted in 17 children. In 15 children it was frequent respiratory diseases that were the first manifestations of the syndrome. In these children the coordination disturbances developed later and showed a slower progress. Early development of atactic symptoms and their rapid progress was observed more frequently in boys. Of the coordination disorders prevalent in 22 patients were symptoms of dynamic ataxia more marked in the arms; in 16 patients these symptoms were combined with noticeable disturbances of the statics. The use of both more complicated and simplified modifications of the coordination tests has made it possible to analyze the structure of the atactic syndrome and to estimate the degree of the compensatory potentialities more precisely.