[Apple Peel syndrome: an uncommon form of intestinal atresia (author's transl)]
Anales Espanoles De Pediatria
|August 1, 1979
Insights
A premature infant with Apple Peel syndrome underwent a two-stage jejunal repair. The infant tolerated oral feedings and achieved satisfactory weight gain, demonstrating a successful surgical outcome.
Area of Science:
- Neonatal surgery
- Pediatric gastroenterology
- Congenital gastrointestinal anomalies
Background:
- Apple Peel syndrome is a rare congenital intestinal obstruction.
- Surgical intervention is necessary for affected neonates.
Observation:
- A premature female infant presented with Apple Peel syndrome.
- The infant weighed 1,800 g at presentation.
Findings:
- A two-stage surgical approach involving jejunoplasty and anastomosis was performed.
- The infant received 55 days of total parenteral nutrition.
- Oral feedings were successfully initiated with good tolerance and weight gain.
Implications:
- This case highlights the successful management of Apple Peel syndrome in a premature infant.
- Jejunal reconstruction can lead to favorable long-term outcomes.
- Early diagnosis and surgical intervention are crucial for improving prognosis.
Abstract:
A case of Apple Peel syndrome in a 1,800 g. premature female infant is reported. In a two stage approach, the dilated proximal segment of the jejunum was treated with jejunoplasty and termino-terminal anastomosis. After 55 days of total parenteral nutrition, oral feedings were instituted with good tolerance and satisfactory weight gain. Five months postoperatively, her weight is 5,500 g. and is on a standard diet for her age.
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