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Surgical correction of caudal duplication
Journal of Pediatric Surgery
|October 1, 1979
Insights
This case report details a rare dipygus monster with an omphalocele and accessory pelvis. Surgical repair was complicated by infections and organ dysfunction, leading to the infant's death.
Area of Science:
- Medical Case Report
- Congenital Abnormalities
- Pediatric Surgery
Background:
- Dipygus is an extremely rare congenital malformation characterized by duplication of the lower body.
- This report presents a unique case of dipygus with associated anomalies requiring surgical intervention.
Observation:
- The infant presented with a dipygus monster, omphalocele, a secondary pelvis with two limbs, an accessory pelvic kidney, and two bladders.
- Surgical intervention involved the removal of the secondary pelvis and extremities, and omphalocele repair.
Findings:
- Postoperative complications included wound infection, urinary tract infections, proteinuria, cardiomegaly, and renovascular hypertension.
- The infant ultimately succumbed to complications following a right nephrectomy, five months after the initial surgery.
Implications:
- This case highlights the complex management challenges associated with severe congenital malformations like dipygus.
- Understanding the spectrum of anomalies and potential complications is crucial for surgical planning and patient care in such rare conditions.
Abstract:
The authors report the rare case of a dipygus monster. The infant had an omphalocele, a secondary pelvis with two limbs, an accessory pelvic kidney, and two bladders. At operation, the secondary pelvis and extremities were removed, and the omphalocele was repaired. The postoperative course was complicated by wound infection, urinary infections, proteinuria, cardiomegaly, and hypertension of renovascular origin. The infant died after right nephrectomy, 5 mo after the first operation.