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[Bile plug syndrome. A rare cause of curable cholestatic jaundice in the infant]
Insights
A rare bile plug in the ampulla of Vater caused cholestatic jaundice in an infant. Surgical removal via a transduodenal approach successfully treated the condition.
Area of Science:
- Pediatric Gastroenterology
- Hepatology
- Surgical Innovation
Background:
- Cholestatic jaundice in infants can stem from various biliary obstructions.
- Bile plug syndrome is a rare but significant cause of extrahepatic biliary obstruction.
Observation:
- An eight-week-old infant presented with severe cholestatic jaundice.
- A distinct bile plug was identified within the ampulla of Vater.
Findings:
- The bile plug was successfully removed using a transduodenal approach.
- This intervention resolved the cholestatic jaundice.
Implications:
- Highlights the importance of considering bile plug syndrome in infant cholestasis.
- Demonstrates the efficacy of the transduodenal approach for bile plug removal.
- Differentiates bile plug syndrome from inspissated bile syndrome in hepatocellular disease.
Abstract:
An eight week old baby who presented with a cholestatic jaundice had a bile plug in the ampulla of Vater. The plug was removal via a transduodenal approach. The bile plug syndrome is a rare cause of extrahepatic biliary cholestasis and is different from the inspissated bile syndrome in which the involvement is predominantly hepatocellular.