Management of pulmonary atresia

Based on experience with 48 patients, a new simple classification of pulmonary atresia, according to pulmonary artery development is suggested. The need for extensive investigation including biplane aortography and right ventricular angiocardiography is emphasized. Adequate display of the anatomy is required to plan the surgical management. Early palliative procedures are advised for hypoxia and later radical correction is possible in a large number of these patients.