[Case of an operated patient with congenital localized supravalvular and valvular aortic stenosis]

The authors presented a rare case with localised congenital supravalvular aortic stenosis associated with bicuspid aortic valvular stenosis which has been surgically treated. The clinical diagnosis was suggested in the presented patient by typical "elfin" face and conformed by left cardiac catheterisation and angiography. The operative procedure with cardiopulmonary by pass consisted of longitudinal aortotomy and insertion of Dacron prosthesis. In addition "open" commissurotomy of partially fused commissures of the bicuspid aortic valve was done. This effectively released the obstruction and enlarged the orifice. The postoperative course was uneventful.