[Angioblastomas, their special forms and rare locations]

Sorting over of our angioblastoma cases occurring in the period from 1954 to 1977 was carried out under the aspect of special forms and rare localisations. Among a total of 93 angioblastomas in 66 patients, there were 81 infratentorial (60 patients), 5 supratentorial (5 patients), and 7 spinal (4 patients) angioblastomas. For 8 of the infratentorial angioblastomas a participation of the brain stem was found; their prognosis was unfavourable and all these patients died. Angioblastomas occurring in a multiple manner are also involving problems unless they are restricted to the cerebellar spheres and the vermis of the cerebellum. In this group there were 37 angioblastomas occurring in 10 patients with an increased familial occurrence in four cases and a systematic affection with angiomatosis retinae in five patients. Four of these patients also died. The large number of 5 angioblastomas of the cerebrum has induced us to study these cases particularly critically. There was a good prognosis for all these cases; they all were solitary tumours (2 solid tumours and 3 typical large-syctic angioblastomas). The prognosis of the spinal angioblastomas of which 7 were found in 4 patients, is dependent upon location and the question of the systematised affection. Remarkably large is the number of young angioblastoma carriers. All 5 cerebral angioblastomas and 6 cerebellar angioblastomas were found in patients below the age of 18. From these findings conclusions can be drawn with regard to an optimisation of an early detection and the exact angiographic clarificatior in order to avoid unnecessary losses due to transfers being carried out too late and, on the other hand, to sort out inoperable findings.