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The left aortic arch and right descending aorta
The British Journal of Radiology
|November 1, 1977
Summary
Congenital left aortic arch with right descending aorta can present in infancy. While radiological appearances may be similar even in acquired cases, aortography is essential for definitive diagnosis.
Area of Science:
- Cardiovascular imaging
- Pediatric radiology
- Thoracic anomalies
Background:
- A left aortic arch with a right descending aorta is a rare congenital anomaly.
- Understanding its presentation in infancy is crucial for timely diagnosis and management.
- Differentiating congenital from acquired forms can be challenging.
Observation:
- This report details three infant cases with left aortic arch and right descending aorta.
- One case involved an acquired abnormality, mimicking congenital presentations.
- Radiological findings were notably similar across all presented cases.
Findings:
- The barium swallow's diagnostic utility in these cases is evaluated.
- Similar radiological appearances were observed in both congenital and acquired instances.
- Aortography is identified as the definitive diagnostic modality.
Implications:
- Accurate diagnosis of aortic arch anomalies is critical for pediatric surgical planning.
- Radiologists should consider both congenital and acquired causes for this vascular ring.
- Advanced imaging like aortography ensures precise anatomical definition for intervention.