[Atypical pulmonary localization of Takayasu's disease]

Takayasu's disease preferentially involves the aorta and its branches. Extension along the pulmonary artery is much more rare. The case presented here is that of a young woman presenting with bilateral involvement of the pulmonary arteries, consisting of hypoplasia on the right and dilatation on the left. The investigation was completed by a study of the collateral vascularization in the right lung and by a lung scan. Right ventricular failure was the condition which led to the diagnosis of the disease. The abdominal aorta and the right renal artery are also involved, which led us to consider the pulmonary lesions as being part of Takayasu's disease. The aortic and renal involvements were asymptomatic and there were no signs of progression of the disease.