[Arrhythmogenic dysplasia of the right ventricle. Description of a case]

A 43 year old man was admitted to our Clinic because of recurrent episodes of palpitation. The electrocardiogram showed incomplete right bundle branch block, frequent ventricular extrasystoles with left bundle branch block morphology and negative T waves in the precordial leads. Two dimensional echocardiography showed marked right ventricular dilatation and right ventricular radionuclide angiography located the enlargment in the infundibulum. Arrhythmogenic right ventricular dysplasia was then suspected. Cardiac angiography excluded the other most common causes of right ventricular dilatation and confirmed the diagnosis. Arrhythmogenic right ventricular dysplasia should thus be regarded as a possible cause of ventricular arrhythmias of unknown etiology.