[Tuberous sclerosis and lymphangiomyomatosis syndrome. Problem of their relationship (author's transl)]

Discussion of a case relating to a patient affected by a typical tuberous sclerosis, and a lymphangiomyomatosis syndrome, proliferation of unstriated muscles of lymphatic system. These symptoms induce pulmonary injuries, ascites and renal angiomyolipomas. The closeness of these localizations with the visceral manifestations of tuberous sclerosis leads to debate connections among the two diseases.