Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Related Experiment Videos

[Diffuse interstitial pulmonary amyloidosis (author's transl)].

F Vilde, N Diebold, A Tenaillon

    La Semaine Des Hopitaux : Organe Fonde Par L'Association D'Enseignement Medical Des Hopitaux De Paris
    |May 8, 1981
    PubMed
    Summary
    This summary is machine-generated.

    Related Concept Videos

    You might also read

    Related Articles

    Articles linked to this work by shared authors, journal, and citation graph.

    Sort by
    Same author

    Design of an electrospun tubular construct combining a mechanical and biological approach to improve tendon repair.

    Journal of materials science. Materials in medicine·2022
    Same author

    Early and systematic administration of fibrinogen concentrate in postpartum haemorrhage following vaginal delivery: the FIDEL randomised controlled trial.

    BJOG : an international journal of obstetrics and gynaecology·2021
    Same author

    [A new case of rare erythrocytosis due to EGLN1 mutation with review of the literature].

    La Revue de medecine interne·2020
    Same author

    [Diagnostic workup in front of an atypical non hemolytic anemia].

    La Revue de medecine interne·2018
    Same author

    Can point-of-care ultrasound predict spinal hypotension during caesarean section? A prospective observational study.

    Anaesthesia·2017
    Same author

    Impact of sleep deprivation on anaesthesia residents' non-technical skills: a pilot simulation-based prospective randomized trial.

    British journal of anaesthesia·2017
    Same journal

    [Dizziness, lipothymia, syncope; symptomatology and therapy].

    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris·2014
    Same journal

    [Antral reaction; its semeiologic value in ulcers of the lesser curvature].

    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris·2014
    Same journal

    [Electrocardiographic and anatomoclinical collation in a case of infarct Tn type].

    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris·2014
    Same journal

    [Are there dissociated forms of hypocorticalism; biogram in chronic adrenal insufficiency].

    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris·2014
    Same journal

    Paradoxical blood pressure collapse and sudden death in paroxysmal arterial hypertension linked to adrenal paraganglioma.

    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris·2010
    Same journal

    Paroxysmal arterial hypertension by adrenal paraganglioma.

    La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris·2010
    See all related articles

    This study reports a rare case of diffuse interstitial pulmonary amyloidosis in a 56-year-old woman. The condition led to respiratory failure and death, highlighting the aggressive nature of this uncommon amyloidosis variant.

    Area of Science:

    • Pulmonary Medicine
    • Pathology
    • Immunology

    Background:

    • Amyloidosis is a group of diseases characterized by the deposition of amyloid proteins in various organs.
    • Pulmonary amyloidosis can manifest in nodular or diffuse interstitial forms, with the latter being exceptionally rare.
    • Diffuse interstitial pulmonary amyloidosis often presents with progressive dyspnea and restrictive or mixed ventilatory defects.

    Observation:

    • A 56-year-old woman presented with dyspneic symptoms, ultimately diagnosed with diffuse interstitial pulmonary amyloidosis.
    • Lung biopsy revealed extensive amyloid infiltration of the lung parenchyma, causing reticulonodular lesions.
    • The patient exhibited a mixed restrictive and obstructive ventilatory deficiency and significant hypogammaglobulinemia.

    Findings:

    Related Experiment Videos

    • Pathological examination confirmed massive amyloid infiltration in the lungs, with minimal involvement of the heart, mediastinal lymph nodes, kidneys, and spleen.
    • Immunofluorescence studies were performed on the pulmonary amyloid deposits.
    • The etiology of this specific case of pulmonary amyloidosis remained undetermined.

    Implications:

    • This case underscores the rarity and distinct pathological features of diffuse interstitial pulmonary amyloidosis compared to nodular forms.
    • The findings emphasize the need for thorough investigation in unexplained hypogammaglobulinemia and respiratory compromise.
    • Further research into the pathogenesis and treatment of diffuse interstitial pulmonary amyloidosis is warranted due to its severe prognosis.