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Progressive myelopathy due to sarcoid.
Clinical Neurology and Neurosurgery
|January 1, 1980
Summary
This case study highlights spinal cord sarcoidosis, a rare neurological condition. Elevated cerebrospinal fluid IgG in CNS sarcoidosis is a significant diagnostic indicator, observed in most previously reported cases.
Area of Science:
- Neurology
- Immunology
- Pathology
Background:
- Sarcoidosis is a multisystem inflammatory disease.
- Neurological involvement, particularly spinal cord sarcoidosis, is rare.
- This study presents a case of progressive paraparesis secondary to spinal sarcoidosis.
Observation:
- A patient presented with progressive paraparesis following uveitis and parotitis.
- Lung biopsy confirmed sarcoidosis.
- Cerebrospinal fluid analysis revealed elevated protein, pleocytosis, and low glucose.
Findings:
- Despite normal myelograms, a diagnosis of spinal cord sarcoidosis was established.
- The patient exhibited elevated cerebrospinal fluid (CSF) IgG.
- CSF globulin elevation, including IgG, was noted in 14 of 15 previously reported CNS sarcoidosis cases.
Implications:
- Elevated CSF IgG may be a common finding in neurosarcoidosis.
- This case underscores the importance of considering sarcoidosis in the differential diagnosis of myelopathy.
- Further research into CSF biomarkers for neurosarcoidosis is warranted.