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Granular cell myoblastoma of the bronchus in a child: a case report
The Japanese Journal of Surgery
|March 1, 1981
Insights
A rare granular cell tumor in a child
Area of Science:
- Pediatric Oncology
- Thoracic Surgery
- Pulmonology
Background:
- Granular cell tumors (GCTs) are rare neoplasms, typically benign, with a predilection for the head and neck region.
- GCTs of the bronchus are exceptionally uncommon, particularly in pediatric patients.
Observation:
- A 5-year-old girl presented with a granular cell myoblastoma obstructing the right main bronchus and extending into the lower trachea.
- Complete bronchial occlusion led to pulmonary suppuration.
Findings:
- Histological diagnosis was confirmed via bronchoscopic biopsy.
- Surgical resection (right pneumonectomy) was performed to manage the pulmonary complication.
- Adjuvant therapy with external radiotherapy and interstitial brachytherapy effectively controlled residual tumor growth.
Implications:
- This case highlights the possibility of GCTs in pediatric airway obstruction.
- Multimodal treatment including surgery and radiotherapy can achieve long-term disease control.
- Successful management in this young patient suggests a favorable prognosis with timely intervention.
Abstract:
Granular cell myoblastoma of of the right main bronchus in a 5-year-old girl is reported. The tumor extended to the lower trachea from the right main bronchus which was occluded completely by the tumor. The diagnosis was established histologically by a obtaining bronchoscopic biopsy specimen. Right pneumonectomy was carried out to control pulmonary suppuration caused by the tumor obstruction of the bronchus. External radiotherapy and interstitial brachytherapy were successful to control the growth of the residual tumor. She has been free from symptoms for about 12 years after the treatment.