Association of carcinoid with neurofibromatosis

Patients with neurofibromatosis have a predilection for other types of tumors. We have described a case of carcinoid tumor of the ampulla of Vater in a patient with extensive cutaneous neurofibromatosis and visceral involvement limited to the heart. A review of the literature as to the types of tumors associated with neurofibromatosis and of several similar cases suggests that carcinoid tumors should be prominently featured among those found in conjunction with the disease.