[Granulomatous Sézary syndrome with epithelial islands]

In a 53-year-old man with Sézary's syndrome, histology showed unique epithelial islands originating from the sweat glands, epithelioid granulomas with giant cells in lymph nodes, and abundant foam cells in the papillary layer as well as perivascularly in the upper dermis and lymph nodes. Severe cholestatic granulomatous hepatitis and hyperlipoproteinemia caused further aggravation of the disease.