[Therapy of calculus-induced hematuria in hemophilia A]

In a patient with haemophilia A who had a staghorn calculus with recidive haematuria nephrectomy was performed without complications. The operation was preceded by compensation for the haemostasis deficiency by substitution of coagulation factor concentrates. Substitution therapy in connection with operations is discussed and obligatory surgical and haemostaseological preconditions are stated.