Paravenous pigmentary retinochoroidal atrophy

Three cases with ophthalmoscopic findings of paravenous pigmentary retinochoroidal atrophy are described. One case had markedly abnormal electrophysiologic studies suggestive of a hereditary chorioretinal degeneration. The other two cases did not. Similarly conflicting results are found in the literature. Because of the great similarity in clinical appearance we none the less feel that all of these cases represent a distinct hereditary disease entity and are not acquired.