The airway of patients with a lipid storage disease

There have been no previous reports in the anaesthetic literature regarding the airway management during anaesthesia of patients with a lipid storage disease. In a 40-year period (1942-1982) at a busy paediatric hospital 15 patients with a lipid storage disease were anaesthetised on 19 occasions. Eight patients were intubated, three of them twice. No difficulties in airway management during anaesthesia were documented.