CT manifestation of ocular muscular dystrophy

Common varieties of muscular dystrophy rarely involve the extraocular muscles, but several uncommon varieties do. In one of our patients with ocular muscular dystrophy (Von Graefe's disease), computed tomography demonstrated atrophy of the extraocular muscles, particularly of the lateral rectus muscles. Involvement of the extraocular muscles by muscular dystrophy has not been previously reported or demonstrated in the radiological literature.