Clear-cell sarcoma of the kidney seen in a 3-day-old newborn

A case of clear-cell sarcoma of the kidney seen in a 3-day-old baby is reported. Resection of the right kidney with tumour and dissection of enlarged lymph nodes were followed by chemotherapy with Vincristine. No radiotherapy was employed. The patient has been living to date without recurrence or metastasis one year after surgery. Favourable outlook of renal neoplasms in the newborn was discussed.