McCune-Albright syndrome (fibrous dysplasia) associated with an orbital tumor

Craniofacial fibrous dysplasia has rarely been described in the polyostotic form of McCune-Albright disease. The unique ophthalmic features of interest in this patient with McCune-Albright's disease was the presence of an orbital tumor that suddenly increased in size compressing the optic nerve. Prompt excision of the tumor resulted in restoration to normal vision.