ABR in patients with congenital/early acquired sensorineural hearing loss, abnormal stapedius reflex thresholds and...

The auditory brain stem response (ABR) was recorded in 14 young subjects with mild to moderately severe congenital/early acquired sensorineural hearing loss and abnormal stapedius reflex thresholds. The speech problems of these patients as evaluated by experienced examiners were considered to be more pronounced than could be explained from the hearing loss as measured by the pure tone audiometry. Psychological testing yielded intelligence scores within normal limits or above average for age in 11. They all gave abnormal ABR, indicating dysfunction of the auditory brain stem pathways or, in a few cases, of the cochlear part of the auditory nerve. Presumably, the electrophysiologically demonstrable pathological changes were caused by perinatal complications or early life infectious disease. ABR may prove valuable in the evaluation of children with speech retardation.