Asymptomatic leiomyosarcoma of maxillary sinus accompanied by primary mucocele

A case of asymptomatic leiomyosarcoma of the maxillary sinus accompanied by primary maxillary mucocele is presented together with a review of the literature. The manifestation and symptoms, pathology in special reference to electron microscopic findings, treatment and prognosis, and origin of this tumor are discussed. Initially, this tumor should be treated by extensive surgical excision, but long-term follow-up is essential in the light of this high rate of local recurrence, and radical neck surgery is indicated for metastatic nodal disease.