[Infrequent digestive pathology associated with a preduodenal portal vein]

We report two cases of preduodenal portal vein (PDPV) has with two different clinical pictures. The first case has an intestinal obstruction in infancy caused by PDPV. In the second child, the PDPV was only an operative finding in the newborn. We report for the first time PDPV associated with Hirschsprung disease.