Urologic management in cloacal dysgenesis

Eleven cases of cloacal dysgenesis from the experience in the Baylor affiliated hospitals from 1969 to 1977 are reviewed. Clinical features including radiographic studies are presented in representative case reports. Despite the initial urgent need for intestinal surgical intervention in these patients, the long-term morbidity and complications are typically related to the genitourinary system. A review of the literature with emphasis on embryogenesis is given. Recommendations for diagnostic approach, and acute and long-term urologic management are made.