[Epidemiology and clinical polymorphism of hereditary ataxia]

The paper is concerned with a clinico-genetical analysis of 66 patients with hereditary ataxia from 44 families. The authors describe typical and atypical variants of separate clinical forms, underline the intra-and interfamilial polymorphism of the clinical picture. The study contains a detailed description of intellectual and extraneuronal changes, a characteristics of the EEG, EMG and REG changes.