[Xanthogranulomathous pyelonephritis (and cystic dysplasia) in a newborn]

The authors present a case of diffuse xanthogranulomatous pyelonephritis in a new-born baby which, according to the literature reviewed, is the youngest case reported throughout the world. They stress the coexistence of two facts not mentioned in the cases reviewed: --Segmentary cystic dysplasia.--Xanthogranulomatous disorder in the suprarenal gland. It is also interesting due to the presence of chronic contralateral pyelonephritis. They comment upon the special features of the etiopathogeny, anatomopathology, clinical picture, diagnosis and treatment of this rare disorder.