Compressive myelopathy in Maroteaux-Lamy syndrome: clinical and pathological findings

A 41-year-old woman with Maroteaux-Lamy syndrome developed spastic tetraparesis due to a compressive cervical myelopathy. There was substantial improvement following laminectomy and excision of the markedly thickened dura. Light and electron microscopic studies showed extensive accumulations of balloon cells in the dura.