[Mesenteric neurofibromatosis. Apropos of a case]

The authors report a case of severe Recklinghausen's disease, revealed early in infancy, by spinal deformities and then by severe dislocations with kypho-scoliosis surgically treated by anterior and posterior fusion. Other localisations of neurofibromatosis were present, especially bones and skin. During the disease's course a wide sub-cutaneous tumor of the chest wall was removed. Two years later a large abdomino-pelvic tumor of the mesentery was discovered and also removed. Histologic examination showed it to be related to Recklinghausen's disease and malignant. The authors analyse the risk of malignant degeneration of this tumor with relation to previous surgical treatment.