Myoclonic ocular jerks

A 39-year-old woman with a familial trait for myoclonic jerks of the neck presented with spontaneous 5- to 40-degree single jerks of the eyes, usually upward, each producing a brief interruption in fixation. Eye movement recordings showed the myoclonic ocular jerks to be saccades with variable intersaccadic intervals. Treatment with 6.0 mg per day of clonazepam reduced her symptoms.