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Retroperitoneal leiomyosarcoma. A clinicopathologic analysis of 36 cases
The American Journal of Surgical Pathology
|April 1, 1983
Summary
Retroperitoneal leiomyosarcoma is a rare cancer. This study suggests that tumors measuring at least 7.5 cm with 1 mitosis per 10 high-power fields may metastasize.
Area of Science:
- Oncology
- Pathology
Background:
- Retroperitoneal leiomyosarcoma is a rare malignancy.
- Clinical presentation is often nonspecific, including pain, weight loss, and abdominal mass.
Purpose of the Study:
- To analyze clinicopathologic features of retroperitoneal leiomyosarcoma.
- To identify potential indicators of malignancy and metastasis.
Main Methods:
- Retrospective clinicopathologic study of 36 retroperitoneal leiomyosarcoma cases.
- Analysis of clinical presentation, gross tumor characteristics, and microscopic findings.
Main Results:
- The study included 24 females and 12 males, aged 12-94 years (median 60).
- Tumor sizes ranged from 7.5 to 35 cm (median 12.8 cm).
- Of 30 patients with follow-up, 77% died of the disease.
Conclusions:
- Retroperitoneal smooth muscle tumors measuring at least 7.5 cm with 1 mitosis/10 HPF may metastasize.
- Establishing absolute minimal criteria for malignancy diagnosis remains challenging.