Incontinentia pigmenti achromians (Ito)

Three children had incontinentia pigmenti achromians (IPA). A study of these cases, together with a review of 70 previously documented cases, suggests that this dermatosis is closely related to systematized depigmented nevus and should be categorized as one of the congenital neurocutaneous diseases. There is also a relationship between IPA and incontinentia pigmenti.