Staged correction of pulmonary atresia and absent right pulmonary artery

Repair of pulmonary atresia with an extra-anatomic conduit has been difficult in patients with absent central pulmonary arteries. Although several methods have been employed successfully, each has inherent problems. Our technique uses a staged approach to complete pulmonary revascularization using the systemic-pulmonary collateral arteries for reconstruction of the involved lung. In our patient, this type of repair was associated with excellent late postoperative symptomatic and hemodynamic results. Complete revascularization of both lungs during correction of pulmonary atresia may improve the surgical management of this condition.