Pseudotruncus arteriosus: Its occurrence with acquired aortic stenosis in an adult

Prolonged survival with pseudotruncus arteriosus, an extreme variant of Fallot's tetralogy, is unusual. We studied the clinical and pathological findings in an adult with uncorrected pseudotruncus. Longevity may have been related to the presence of markedly enlarged bronchial arteries that provided collateral circulation to the lungs. However, prolonged survival was accompanied by the development of severe degenerative changes of the aortic valve leaflets that resulted in acquired valvular stenosis.