Atypical calcifying epithelial odontogenic tumor of the maxilla

A case of atypical calcifying epithelial odontogenic tumor is reported to show that many different lesions can cause periapical radiolucent areas and to contribute to the expanding histologic spectrum of the calcifying epithelial odontogenic tumor. Methods used in differential diagnosis of radiolucent lesions in the jaws include: comprehensive history, clinical and radiographic examination, tooth vitality tests, laboratory tests, aspiration, and biopsy. To prevent hemorrhage, precautions should be taken before biopsy or surgery to rule out a vascular lesion. Proper treatment of odontogenic tumors requires thorough removal of the tumor for initial therapy and close, long-term, follow-up observation to check for recurrence.