[Cerebrovascular disease and pseudoxanthoma elasticum: apropos of a case]

The authors review the case of a girl affected by pseudoxanthoma elasticum, that twice experienced at 11 and 14 years recurrence of stroke in the field of the right carotid artery. Angiographic examination disclosed hypoplasia of the right internal carotid artery, in it's extra-cranial tract. After having reviewed the literature about the subject, the authors debate the possible pathogenetic mechanisms and eventually favour a recurrent thrombo-embolic event. This statement might have surgical therapeutic implications.