True hermaphroditism with hydrocolpos

A case of true hermaphroditism with hydrocolpos in a 7-month-old infant is presented. This is, to the authors' knowledge reported case of association of both anomalies. Hydrocolpos is a clinical entity characterized by vaginal distension with accumulation of fluid, which can cause respiratory embarrassment and urinary, intestinal and circulatory obstruction. It is a condition of great rarity. It is usually detected in the neonatal period, although it has been reported in older children, and it calls for urgent treatment. True hermaphroditism is a rare form of intersexuality, which can only be considered to exist if both male and female elements can be identified in the gonad.