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Related Experiment Videos

Cortical deafness in multiple sclerosis

T Tabira, S Tsuji, T Nagashima

    Journal of Neurology, Neurosurgery, and Psychiatry
    |May 1, 1981
    PubMed
    Summary

    Multiple sclerosis can cause cortical deafness, a rare condition originating in subcortical white matter. This patient experienced full hearing recovery after auditory agnosia and pure word deafness.

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    Area of Science:

    • Neurology
    • Neuroscience
    • Otolaryngology

    Background:

    • Multiple sclerosis (MS) is a demyelinating disease affecting the central nervous system.
    • Auditory pathway involvement in MS is uncommon, with cortical deafness being exceptionally rare.

    Observation:

    • A patient with multiple sclerosis presented with sudden, profound bilateral hearing loss.
    • Initial symptoms included auditory agnosia and pure word deafness, indicating higher-level auditory processing deficits.
    • Otological and neurophysiological assessments were crucial for diagnosis.

    Findings:

    • Lesions were identified in the subcortical white matter, suggesting a non-cortical origin for the deafness.
    • Complete recovery of hearing function was observed.
    • The patient's auditory agnosia and pure word deafness resolved spontaneously.

    Implications:

    • This case highlights the potential for auditory pathway dysfunction in MS, even with subcortical lesions.
    • The rarity of MS-related cortical deafness underscores the need for comprehensive neurological evaluation in hearing loss cases.
    • A favorable prognosis is possible, emphasizing the importance of early detection and management.

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