Peninsula pupil. Anomaly unique to Newfoundland and Labrador?

Forty cases of an unusual form of iris atrophy that results in a characteristically oval pupil have been seen in Newfoundland and Labrador. The anomaly is an atrophy of part of the sphincter pupillae, is confined to the iris, and is not associated with any systemic disorder. The great majority of those affected are male, and all have blue eyes. We suggest that it may be an inherited trait.