[Malignant lymphoplasmocytic lymphoma of the orbit and conjunctiva (author's transl)]

New functional classifications of malignant lymphomas have demonstrated the relative frequency of malignant lymphoplasmocytic lymphoma of the orbit. The tumors, which show the particular characteristic of secreting monoclonal immunoglobulins, and which may follow a Sjögren's syndrome or a pseudolymphoma, could represent a localized form of Waldenström's disease. They have a relatively favorable prognosis, however, if recognized at a sufficiently early stage.