Tetralogy of Fallot with type C complete atrioventricular canal: surgical repair in three cases

Insights

This study reports successful surgical repair of tetralogy of Fallot with complete atrioventricular canal type C in three infants. The innovative technique achieved satisfactory outcomes, highlighting a viable surgical approach for this complex congenital heart defect.

Area of Science:

  • Cardiovascular Surgery
  • Pediatric Cardiology
  • Congenital Heart Defects

Background:

  • Tetralogy of Fallot (TOF) is a complex cyanotic congenital heart disease.
  • Complete atrioventricular canal (CAVC) type C presents significant surgical challenges, especially when associated with TOF.
  • Successful surgical management of combined TOF and CAVC type C requires precise anatomical understanding and tailored surgical techniques.

Purpose of the Study:

  • To report the successful surgical repair of three consecutive cases of tetralogy of Fallot associated with complete atrioventricular canal type C.
  • To describe the surgical techniques employed for anatomical correction.
  • To evaluate the early postoperative outcomes of this complex congenital heart repair.

Main Methods:

  • Preoperative diagnosis confirmed by right and left ventriculography.
  • Surgical repair involved closure of ventricular septal defects with Dacron patches.
  • Reconstruction of atrioventricular valves using native tissue and precise suture placement.
  • Relief of right ventricular outflow tract obstruction via infundibulectomy, pulmonary valvulotomy, and patch augmentation or valved conduit placement.

Main Results:

  • Successful biventricular repair was achieved in all three patients.
  • Postoperative conditions were satisfactory at six months.
  • Patients' medical management varied, with one on digitalis, another on digitalis and diuretics, and the third requiring no medication.

Conclusions:

  • The study demonstrates the feasibility and success of surgical repair for the rare combination of tetralogy of Fallot and complete atrioventricular canal type C.
  • The described surgical modifications for atrioventricular valve reconstruction and septal defect closure are effective.
  • Satisfactory early outcomes suggest this approach offers a viable treatment option for this complex pediatric cardiac condition.