Generous craniectomy for Kleeblattschädel anomaly

In the case presented, Kleeblattschädel, or cloverleaf skull deformity, was treated successfully with a two-staged, generous craniectomy. The pertinent aspects of this rare anomaly are reviewed in light of information from other cases described previously. The present case illustrates that an early surgical approach of subtotal calvariectomy may improve the commonly predicted poor prognosis in patients with Kleeblattschädel anomaly if the clinical severity of the disease is not immediately overwhelming.