[Lymphangioleiomyomatosis. Problems in differential diagnosis, etiology and prognosis (author's transl)]

Four different cases (diffuse interstitial lung fibrosis with leiomyomatosis, Lymphangioleiomyomatosis of the lung, fibroleiomyoma of the lung and adenomyofibroma of the lung) are presented and the differential diagnostic criteria are discussed. On survey of the literature on Lymphangioleiomyomatosis it is concluded that so far this diagnosis seems ill defined. As it cannot be excluded that the cases described so far represent an assortment of various diseases with different etiology, the authors believe that it is impossible to give a reliable statement on prognosis either for the condition in general or for an individual case.