Congenital diverticulum of the left ventricle extending into exomphalos

Ventricular diverticulum in association with exomphalos is rare. It is usually accompanied by split sternum, anterior pericardial and diaphragmatic defects and intracardiac abnormalities. This paper reports a neonate who presented with exomphalos and was noted to have a pulsating vessel, on the superior margin of the sac, which proved to be a left ventricular diverticulum. The successful correction is described.