Paratesticular neuroblastoma associated with subependymal giant cell astrocytoma

We describe a case of neuroblastoma presenting as a paratesticular mass in infancy. To our knowledge this is the first case of a paratesticular neuroblastoma reported in the literature. An operation combined with radiotherapy and chemotherapy has achieved long-term survival despite obvious multifocal disease. Seven years after treatment of the inital tumor the patient presented with a subependymal giant cell astrocytoma, an extremely rare neuroectodermal tumor. Discussion is directed to possible explanations for this unusual case of multifocal, metachronous neuroectodermal neoplasms.