Heterotopic gastric tissue of the bile duct

A unique heterotopia of the main hepatic duct causing episodic jaundice in a young man is described. The clinical presentation, radiologic diagnosis, and histologic findings are presented, as well as the possible embryologic etiology. Extensive review of the literature indicates that this case is unique. Although heterotopic gastric tissue previously has been found in the gallbladder, none has been reported in the extrahepatic bile ducts.