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[Arrhythmogenic right ventricle]
J Kajzr1, J Bastecký, J Kvasnicka
1I interní klinika FN, Hradec Králové.
Vnitrni Lekarstvi
|August 1, 1995
Summary
This study details a case of arrhythmogenic right ventricle (ARV) diagnosed in a young patient presenting with recurrent ventricular tachycardia and heart failure. Effective management involved a combination of medications and cardiac pacing.
Area of Science:
- Cardiology
- Electrophysiology
- Genetics
Background:
- Arrhythmogenic right ventricle (ARV) is a hereditary heart muscle disease.
- It is characterized by fibrofatty replacement of the right ventricular myocardium.
- ARV can lead to ventricular arrhythmias, heart failure, and sudden cardiac death.
Observation:
- A 26-year-old patient presented with recurrent ventricular tachycardia and dextrolateral cardiac failure.
- Other potential causes including pulmonary embolism, ischemic heart disease, and Ebstein's anomaly were excluded.
- Diagnostic findings included negative T waves in V1-V3 during sinus rhythm and specific QRS complex morphology during tachycardia.
Findings:
- The diagnosis of arrhythmogenic right ventricle was established based on clinical presentation and diagnostic criteria.
- Electrocardiography revealed characteristic T wave inversions and QRS abnormalities suggestive of right bundle branch block.
- Angiography showed marked trabeculization and impaired right ventricular outflow tract kinetics, further supporting the ARV diagnosis.
Implications:
- Simultaneous administration of beta-blockers, Cordarone, and cardiac stimulation (AAI) proved effective in preventing ventricular tachycardia relapses.
- This case highlights the importance of early diagnosis and comprehensive management strategies for ARV.
- Further research into genetic factors and long-term outcomes in ARV patients is warranted.