[Ehlers-Danlos syndrome with giant duodenal diverticulum as a cause of cholangitis]

The case of a patient with the Ehlers-Danlos syndrome who presented a picture of acute cholangitis only attributable to the presence of a large duodenal diverticulum is reported. The pathologic implications of the duodenal diverticula are described with special attention being given to their participation in the development of acute cholangitis. The digestive manifestations associated to the Ehlers-Danlos syndrome are also reviewed.